Ivemark Syndrome- A Rare Syndrome with Constellation of Anatomical Defects
نویسندگان
چکیده
Ivemark syndrome is classified as a heterotaxy disorder or a laterality disorder. These terms refer to the failure of the internal organs of the chest and abdomen to be arranged in the proper location within the body. It is characterized by the absence (asplenia) or underdevelopment (hypoplasia) of the spleen, malformations of the heart and the abnormal arrangement of the internal organs of the chest and abdomen. We report a 7 day old female neonate with this syndrome with complex congenital cardiac defects with right isomerism with asplenia with midline liver.
منابع مشابه
Ivemark syndrome-a rare entity with specific anatomical features.
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